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Table 2B Results prolonged exercise test subject 2.

From: Prolonged exercise testing in two children with a mild Multiple Acyl-CoA-Dehydrogenase deficiency

  T = 0 T = 30 T = 60 T = 75 T = 90 T = 120
HR (b·min-1) 80 120 120 120 120  
VO2 (ml·min-1) 260 450 620 620 600  
RER (VCO2·VO2-1) 0.9 0.9 0.95 0.95 0.9  
Glucose (mmol·l-1) 5.2 4.6 4.3 4.4   4.5
Lactate (mmol·l-1) 2.0 0.9 0.9 1.0   1.2
CK (u·l-1) 58   80 78   78
3-keto-B (mmol·l-1) <0.05 <0.05 0.07    0.14
3-OH-B (mmol·l-1) <0.02 <0.02 0.04    0.24
FFA (umol·l-1) 0.15 0.31 0.62 0.91   1.34
Urine       
Ethylmalonic acid in mmol·mol-1 creatinine T = -60–0: 29      T = 120–300: 59
  1. Abbreviations: HR: heart rate, RER: Respiratory Exchange Ratio, VO2: oxygen uptake, CK: creatine kinase, 3-keto-B: 3-ketobutyric acid, 3-OH-B: 3-hydroxybutyric acid, FFA: Free Fatty Acids.