Skip to main content

Table 2A Results prolonged exercise test subject 1

From: Prolonged exercise testing in two children with a mild Multiple Acyl-CoA-Dehydrogenase deficiency

  T = 0 T = 30 T = 60 T = 75 T = 90 T = 120
HR (b·min-1) 70 140 145 145 150  
VO2 (ml·min-1) 300 700 700 720 720  
RER (VCO2·VO2-1) 0.8 0.95 0.95 0.9 0.9  
Glucose (mmol·l-1) 7.1 5.6 4.9 4.8 5.5 4.8
Lactate (mmol·l-1) 1.1 1.2 1.0 1.3 1.1 1.0
CK (u·l-1) 103   98 105 119 117
3-keto-B (mmol·l-1) 0.07 <0.05 <0.05 0.05 0.1 0.15
3-OH-B (mmol·l-1) 0.09 <0.02 <0.02 0.05 0.12 0.26
FFA (umol·l-1) 0.76 0.28 0.49 0.88 1.03 0.93
Urine       
Ethylmalonic acid in Mmol·mol-1 creatine T = -60–0: 16      T = 120–300: 74
  1. Abbreviations: HR: heart rate, RER: Respiratory Exchange Ratio, VO2: oxygen uptake, CK: creatine kinase, 3-keto-B: 3-ketobutyric acid, 3-OH-B: 3-hydroxybutyric acid, FFA: Free Fatty Acids.